Protein / target

Dystrophin

DMDP11532Homo sapiensSwiss-Prot
Clinically validated
Therapeutic maturity
5
Approved medicines
2
Clinical trials
Antibody-tractable
Druggability
GO CC high conf

Protein at a glance

Biological role

Structural constituent of cytoskeleton

Primary system

Nervous system

Strongest disease association

neuromuscular disease caused by qualitative or quantitative defects of dystrophin

Genetic evidence · score 0.93

Therapeutic maturity

Clinically validated target

5 approved medicines against this target

Druggability

Antibody

Open Targets tractability · GO CC high conf

Clinical development

5 approved · 2 in clinical development

2 linked trials

Research activity

Emerging research

3 papers · latest 2025

Derived from structured UniProt, Open Targets and literature data on this page.

Protein profile

UniProt 2026_02

Canonical identity and biological annotation from UniProt.

Function

Anchors the extracellular matrix to the cytoskeleton via F-actin. Ligand for dystroglycan. Component of the dystrophin-associated glycoprotein complex which accumulates at the neuromuscular junction (NMJ) and at a variety of synapses in the peripheral and central nervous systems and has a structural function in stabilizing the sarcolemma. Also implicated in signaling events and synaptic transmission

Subcellular location

Cell membrane, sarcolemmaCytoplasm, cytoskeletonPostsynaptic cell membrane
Domains and Gene Ontology detail (55)

Domains & features

Calponin-homology (CH) 1Calponin-homology (CH) 2WW

Gene Ontology

  • Ccell surface
  • Ccell-substrate junction
  • Ccostamere
  • Ccytoskeleton
  • Ccytosol
  • Cdystrophin-associated glycoprotein complex
  • Cfilopodium
  • Cfilopodium membrane
  • Cmembrane raft
  • Cneuron projection terminus
  • Cnucleus
  • Cplasma membrane

3685 aa · 427 kDa · 17 isoforms

Biological roles

Reactome v97

What this protein does, drawn together from its UniProt function, Gene Ontology terms and Reactome pathways.

Synaptic signallingUniProt · GOMuscle contractionGO · ReactomeIon channel gatingGOCell adhesionUniProt
View supporting evidence

Synaptic signalling

  • ·Anchors the extracellular matrix to the cytoskeleton via F-actin. Ligand for dystroglyca…
  • ·Postsynaptic cell membrane
  • ·postsynaptic membrane
  • ·synapse

Muscle contraction

  • ·myosin binding
  • ·cardiac muscle contraction
  • ·regulation of cardiac muscle contraction by regulation of the release of sequestered cal…
  • ·regulation of skeletal muscle contraction

Ion channel gating

  • ·regulation of calcium ion transmembrane transport
  • ·regulation of sodium ion transmembrane transport

Cell adhesion

  • ·Anchors the extracellular matrix to the cytoskeleton via F-actin. Ligand for dystroglyca…
View underlying pathways (3)

Concepts derived from UniProt GO Reactome — each badge above shows which sources supported that role.

Interaction neighbourhood

STRING v12.0

Proteins with the strongest functional or physical association. Node size and line weight reflect STRING confidence; hover or select a partner to inspect one association.

DAG1SSPNSNTA1SNTB1SGCDSGCAUTRNSNTG1SGCBCAV3DMD

10 strongest partners — larger node and heavier line mean higher confidence

Functional and physical associations from STRING v12.0. Only associations with this protein are drawn — partner-to-partner links are not part of this evidence.

Drugs targeting this protein

1

Whether each drug engages this protein directly or through a complex, and how many other targets are recorded for it. Direct binders with few recorded targets are listed first.

delandistrogene moxeparvovec
Narrow target profileApprovedExogenous gene

Dystrophin exogenous gene

Appears in clinical studies involving Becker muscular dystrophy, Duchenne muscular dystrophy, Duchenne muscular dystrophy, Duchenne muscular dystrophy

Direct interaction with this protein · Only this protein recorded as a target

ChEMBL mechanism, action type and target identity. Open Targets clinical status and indications.

Translational evidence

Open Targets 26

Why this target matters therapeutically — disease associations, drugs in development, tractability and safety, from Open Targets.

Strongest genetic associations

Human genetic evidence — the most direct causal link between this target and a disease.

neuromuscular disease caused by qualitative or quantitative defects of dystrophin0.93

Genetic · overall 0.59

dilated cardiomyopathy 3B0.91

Genetic · overall 0.79

Duchenne muscular dystrophy0.91

Genetic · overall 0.87

Abnormality of the cardiovascular system0.91

Genetic · overall 0.55

Becker muscular dystrophy0.90

Genetic · overall 0.82

Highest-confidence therapeutic associations

Diseases where a drug acting on this target has already reached clinical development.

muscular dystrophy0.87

Clinical · overall 0.66

Highest overall evidence

Remaining associations by Open Targets' aggregated evidence score.

familial isolated dilated cardiomyopathy0.63

Genetic literature

progressive muscular dystrophy0.62

Genetic

cardiomyopathy0.55

Genetic

Elevated circulating creatine kinase concentration0.55

Genetic

Show all associations
Duchenne muscular dystrophy0.87
Becker muscular dystrophy0.82
dilated cardiomyopathy 3B0.79
muscular dystrophy0.66
familial isolated dilated cardiomyopathy0.63
progressive muscular dystrophy0.62
neuromuscular disease caused by qualitative or quantitative defects of dystrophin0.59
Abnormality of the cardiovascular system0.55
cardiomyopathy0.55
Elevated circulating creatine kinase concentration0.55

Open Targets ranks 4,815 associations for this target and we store the top 10 by aggregated score. The long tail is largely literature co-mention and RNA-expression evidence, not evidence that this target drives those diseases.

Known drugs · 8 total

DELANDISTROGENE MOXEPARVOVECApproval

Becker muscular dystrophy · Duchenne muscular dystrophy · Duchenne muscular dystrophy

SUVODIRSEN SODIUMUnknown

Duchenne muscular dystrophy

SUVODIRSENPhase 2 3

Duchenne muscular dystrophy · Duchenne muscular dystrophy

ETEPLIRSENApproval

muscular dystrophy · Duchenne muscular dystrophy · Duchenne muscular dystrophy

VILTOLARSENApproval

muscular dystrophy · Duchenne muscular dystrophy · Duchenne muscular dystrophy

GOLODIRSENApproval

muscular dystrophy · Duchenne muscular dystrophy · Duchenne muscular dystrophy

DRISAPERSENPhase 3

Duchenne muscular dystrophy · Duchenne muscular dystrophy

CASIMERSENApproval

muscular dystrophy · Duchenne muscular dystrophy · Duchenne muscular dystrophy

Tractability

AB · GO CC high confAB · UniProt loc med confPR · Database UbiquitinationPR · Half-life Data

Clinical trials

2

Trials of drugs that target this protein — reached indirectly through those drugs, so a trial listed here studies the drug, not the protein.

ClinicalTrials.gov via the drug-target graph.

Research activity

3 papers · to 2025

Papers linked directly to this protein. This is the protein's own literature — descriptor-derived papers are kept separate below.

Most cited

Recent

Europe PMC papers linked directly to this protein.

Forefront confidence

Synthesis

Our own weighting of the evidence behind each disease association. Human genetics and clinical evidence count for most; literature co-mention counts for little, because two entities sharing an abstract is not evidence that one drives the other.

Duchenne muscular dystrophyWell supported
0.99
agreement 0.911.00
Genetic38%Clinical30%Somatic mutation17%Animal model9%Literature6%RNA expression1%Genetic literaturedup

Open Targets aggregate 0.87 · 6 independent evidence families · 1 not counted as duplicate

Becker muscular dystrophyWell supported
0.96
agreement 0.871.00
Genetic51%Clinical26%Animal model18%Literature6%Genetic literaturedup

Open Targets aggregate 0.82 · 4 independent evidence families · 1 not counted as duplicate

muscular dystrophyWell supported
0.95
agreement 0.841.00
Genetic55%Clinical42%Literature3%

Open Targets aggregate 0.66 · 3 independent evidence families

neuromuscular disease caused by qualitative or quantitative defects of dystrophinWell supported
0.94
agreement 0.801.00
Genetic90%Literature10%

Open Targets aggregate 0.59 · 2 independent evidence families

dilated cardiomyopathy 3BWell supported
0.94
agreement 0.821.00
Genetic77%Animal model21%Literature2%Genetic literaturedup

Open Targets aggregate 0.79 · 3 independent evidence families · 1 not counted as duplicate

The evidence agreement range shows how closely the independent evidence families agree — it is not a statistical confidence interval, and nothing here is fitted to outcome data. Derived from Open Targets evidence types under Forefront weighting; the underlying per-type scores are shown above so the calculation can be checked.

What's happening now

1

Recent activity around this target, drawn from one canonical event stream. Every item is reached through a drug that targets this protein, so each event is news about that drug rather than about the protein directly.

  1. New publication2024-10-09
    AAV gene therapy for Duchenne muscular dystrophy: the EMBARK phase 3 randomized trial.

    Nature medicine · 2025 · 107 citations · Europe PMC · via delandistrogene moxeparvovec

Objective event titles are shown unmodified; the event kind and significance line are derived from structured fields. Forefront AttentionEvent stream aggregating Europe PMC Regulatory filings ClinicalTrials.gov.