Back to discover
Disease

Neuromyelitis Optica

Late-stage therapeutic developmentEmerging researchCooling momentum
6
Publications
24
Clinical trials
4
Related conditions
5
Related proteins
2025
Latest publication
Current focus
Aquaporin 4 biologyAutoantibodies biologyTherapeutic developmentInflammation & immunityMetabolic & lifestyle factors
Latest activity
beta

Recent clinical, regulatory, research and industry developments relating to this disease.

Estimated Brain Age in Healthy Aging and Across Multiple Neurological Disorders.

Research2024-11-26Journal of magnetic resonance imaging : JMRI

The function of astrocytes and their role in neurological diseases.

Research2023-10-13The European journal of neuroscience

Approval: Uplizna (EMA)

Regulatory2022-04-25EMA

Approval: Enspryng (EMA)

Regulatory2021-06-24EMA

What's happening now

An analyst briefing on current research, clinical, regulatory and industry activity surrounding this disease.

Clinical Milestones16View all 16
+8 more in the activity timeline below
Activity timeline16

Therapeutic landscape

Therapies with a regulatory footing for this condition, alongside the wider set of agents co-studied with it in the literature.

Approved & established therapies
Inebilizumabapproved

Approval — Uplizna is indicated as monotherapy for the treatment of adult patients with neuromyeliti… (2022)

Satralizumabapproved

Approval — Satralizumab (Enspryng) is indicated as a monotherapy or in combination with immunosuppre… (2021)

Ravulizumabapproved

Approval — Paroxysmal nocturnal haemoglobinuria (PNH)Ultomiris is indicated in the treatment of adul… (2019)

Eculizumabapproved

Accelerated approval — Soliris is indicated in adults and children for the treatment of: Paroxysmal nocturnal h… (2007)

Clinical trials

11 sponsors · 3 new · 4 completed in the last 12 months (net -1)

The current development programme across all trial phases.

Clinical programme
24
All trials
6
Active
18
Late-stage
6
Completed
Late-stage studies
Recently completed

Regulatory timeline

Drug regulatory events matched to this condition by indication — EMA.

First approvals
2022emaApprovalInebilizumab· Uplizna is indicated as monotherapy for the treatment of adult patients with neuromyelitis optica spectrum disorders (NMOSD) who are anti-aquaporin 4 immunoglobulin G (AQP4-IgG) seropositive (see section 5.1). source ↗
2021emaApprovalSatralizumab· Satralizumab (Enspryng) is indicated as a monotherapy or in combination with immunosuppressive therapy (IST) for the treatment of neuromyelitis optica spectrum disorders (NMOSD) in adult and adolescent patients from 12 years of age who are anti-aquaporin-4 IgG (AQP4-IgG) seropositive. source ↗
2019emaApprovalRavulizumab· Paroxysmal nocturnal haemoglobinuria (PNH)Ultomiris is indicated in the treatment of adult and paediatric patients with a body weight of 10 kg or above with PNH:- in patients with haemolysis with clinical symptom(s) indicative of high disease activity.- in patients who are clinically stable after having been treated with eculizumab for at least the past 6 months (see section 5.1). Atypical haemolytic uremic syndrome (aHUS)Ultomiris is indicated in the treatment of patients with a body weight of 10 kg or above with aHUS who are complement inhibitor treatment-naïve or have received eculizumab for at least 3 months and have evidence of response to eculizumab (see section 5.1). Generalized myasthenia gravis (gMG)Ultomiris is indicated as an add-on to standard therapy for the treatment of adult patients with gMG who are anti-acetylcholine receptor (AChR) antibody-positive. Neuromyelitis Optica Spectrum Disorder (NMOSD)Ultomiris is indicated in the treatment of adult patients with NMOSD who are anti-aquaporin 4 (AQP4) antibody-positive (see section 5.1). Ultomiris is indicated in the treatment of adult patients with paroxysmal nocturnal haemoglobinuria (PNH):- in patients with haemolysis with clinical symptom(s) indicative of high disease activity.- in patients who are clinically stable after having been treated with eculizumab for at least the past 6 months. Ultomiris is indicated in the treatment of adult patients with atypical haemolytic uremic syndrome (aHUS) who are complement inhibitor treatment-naïve or have received eculizumab for at least 3 months and have evidence of response to eculizumab. source ↗
2007emaAccelerated approvalEculizumab· Soliris is indicated in adults and children for the treatment of: Paroxysmal nocturnal haemoglobinuria (PNH). Evidence of clinical benefit is demonstrated in patients with haemolysis with clinical symptom(s) indicative of high disease activity, regardless of transfusion history (see section 5.1).  Atypical haemolytic uremic syndrome (aHUS). Soliris is indicated in adults for the treatment of: Refractory generalized myasthenia gravis (gMG) in patients who are anti-acetylcholine receptor (AChR) antibody-positive (see section 5.1). Neuromyelitis optica spectrum disorder (NMOSD) in patients who are anti-aquaporin-4 (AQP4) antibody-positive with a relapsing course of the disease. source ↗

European Medicines Agency (CC BY 4.0). Events are matched to this condition by drug indication text — approvals/updates for drugs indicated for it, not disease-specific acts.

Research activity

6 papers

Key research shaping understanding of this disease, combining the latest publications with the most influential evidence.

Publications over time
20182025
Most influential
Recent publications
Major themes8
  • Neuromyelitis Optica3
  • Multiple Sclerosis2
  • Aging1
  • Alzheimer Disease1
  • Brain1
  • Central Nervous System Diseases1
  • Gastrointestinal Microbiome1
  • Healthy Aging1
Leading journals6
  • Acta neuropathologica1
  • Cells1
  • Journal of magnetic resonance imaging : JMRI1
  • Journal of neurology, neurosurgery, and psychiatry1
  • Scientific reports1
  • The European journal of neuroscience1
Leading researchers8
  • Anderson MR1
  • Aoki M1
  • Bai Y1
  • Barkhof F1
  • Barnett MH1
  • Bilodeau PA1
  • Bobrowski-Khoury N1
  • Brilot F1
Affiliations (unnormalised)6
  • Beijing Tiantan Hospital1
  • Boston Children's Hospital1
  • Brain and Mind Centre1
  • Center for Brain Research1
  • Centre for Medical Image Computing1
  • Children's Hospital1

Disease biology

5 matches

Key proteins & gene products studied in this disease. Number shows shared papers.

Related conditions

4 matches

Diseases frequently studied alongside this one. Number shows shared papers.

Disease profile

A grounded synthesis of the condition — overview, causes, mechanism, risk factors and current standard of care.

Overview

Neuromyelitis optica is a demyelinating and/or necrotizing syndrome of the central nervous system characterized by acute optic neuritis and transverse myelitis. It primarily involves the optic nerves and spinal cord and is associated with specific autoantibodies to aquaporin 4.

Causes

The grounding supports an autoimmune basis, indicated by the presence of specific autoantibodies to aquaporin 4. It also notes co-studied autoantibodies and immunoglobulin G, consistent with an antibody-mediated disease process.

Pathophysiology

The disease is linked to lesions in the optic nerves and spinal cord that are demyelinating and/or necrotizing. Aquaporin 4 is directly implicated, and astrocytes are highlighted as important because aquaporin 4 expression on astrocytes is directly related to neuromyelitis optica. The literature also points to metabolism-related aspects and broader immune and astrocytic mechanisms in related neuroinflammatory disorders.

Current standard of care

The supplied grounding does not provide a clear treatment standard for neuromyelitis optica. Rituximab is co-studied, which suggests interest in B-cell–directed immunotherapy, but the abstracts provided do not establish it as standard of care.

AI-generated summary grounded in MeSH and 2 peer-reviewed sources. Informational only — not medical advice. Generated 2026-07-07.

Reference

Authoritative identity, definition & identifiers.

Defined in MeSH

A syndrome characterized by acute OPTIC NEURITIS; MYELITIS, TRANSVERSE; demyelinating and/or necrotizing lesions in the OPTIC NERVES and SPINAL CORD; and presence of specific autoantibodies to AQUAPORIN 4.

References & data sources
  • Disease identity & definition — NLM Medical Subject Headings (MeSH), public domain
  • Clinical trials — ClinicalTrials.gov (U.S. National Library of Medicine)
  • Research activity — Europe PMC (EMBL-EBI) + OpenAlex-derived paper links
  • Related entities are derived from literature co-mention (studied together) — associative, not causal.