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Disease

Lysosomal Storage Diseases

Clinical development underwayEmerging research
2
Publications
2
Clinical trials
12
Associated genes
9
Related proteins
2023
Latest publication
Current focus
Sphingomyelin phosphodiesterase biologyStearoyl-coa desaturase biologyTherapeutic developmentGenetics & risk factors
Latest activity
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Recent clinical, regulatory, research and industry developments relating to this disease.

What's happening now

An analyst briefing on current research, clinical, regulatory and industry activity surrounding this disease.

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Clinical trials

2 sponsors · 0 new · 0 completed in the last 12 months (net +0)

The current development programme across all trial phases.

Clinical programme
2
All trials
0
Active
0
Late-stage
0
Completed

Research activity

2 papers

Key research shaping understanding of this disease, combining the latest publications with the most influential evidence.

Publications over time
20172023
Most influential
Recent publications
Major themes3
  • Genetic Therapy1
  • Lysosomal Storage Diseases1
  • Quality of Life1
Leading journals1
  • Journal of inherited metabolic disease2
Leading researchers8
  • Aiuti A1
  • Bernardo ME1
  • Bigger B1
  • Calbi V1
  • Ellison S1
  • Fumagalli F1
  • Parker H1
  • Penati R1
Affiliations (unnormalised)4
  • IRCCS San Raffaele Scientific Institute1
  • San Raffaele Telethon Institute for Gene Therapy (SR-TIGET)1
  • University of Manchester1
  • Vita Salute San Raffaele University1

Associated genes

12 matches

Genes associated with this disease in the canonical knowledge graph (Open Targets evidence). Number shows the association score.

Disease biology

9 matches

Proteins whose encoding gene is associated with this disease, reached through the canonical gene→disease graph. Number shows the gene's association score.

Reference

Authoritative identity, definition & identifiers.

Defined in MeSH

Inborn errors of metabolism characterized by defects in specific lysosomal hydrolases and resulting in intracellular accumulation of unmetabolized substrates.

References & data sources
  • Disease identity & definition — NLM Medical Subject Headings (MeSH), public domain
  • Clinical trials — ClinicalTrials.gov (U.S. National Library of Medicine)
  • Research activity — Europe PMC (EMBL-EBI) + OpenAlex-derived paper links
  • Related entities are derived from literature co-mention (studied together) — associative, not causal.